Treatment for HT-1 (hereditary tyrosinemia) involves using the FDA-approved medication nitisinone. It is a synthetic, reversible inhibitor of 4-hydroxyphenylpyruvate dioxygenase, an enzyme producing harmful compounds connected to HT-1. In addition to taking Nitisinone, patients must follow a strict diet restricting their intake of tyrosine and phenylalanine. Report any unexpected eye problems, rashes, jaundice, or substantial bleeding immediately. With a daily dose cap of 2 mg/kg, the dosage of Nitisinone can be adjusted based on how each patient responds to it. Plasma tyrosine levels must be carefully controlled to avoid adverse consequences. With a valid prescription, Nitisinone is easily accessible, and Nitisinone price in India. It should be started under a doctor's supervision and is simple to include in daily activities.